Acute Nutritional Ketosis in VLCAD Deficiency
Conditions
- VLCAD Deficiency
- Fatty Acid Oxidation Defects
Interventions
- DIETARY_SUPPLEMENT: ketone ester drink
- BEHAVIORAL: exercise
- PROCEDURE: muscle biopsy
- DIAGNOSTIC_TEST: Magnetic Resonance Imaging
Sponsor
University Medical Center Groningen
Collaborators
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